{"id":"aa5b1121838b","type":"article","url":"https://hartvaat.nl/2018/12/04/echocardiografische-screening-op-ph-bij-aangeboren-hartafwijkingen-jacc-review/","title":"Echocardiografische screening op PH bij aangeboren hartafwijkingen: JACC review","title_en":"Echocardiographic Screening for Pulmonary Hypertension in Congenital Heart Disease: JACC Review Topic of the Week.","category":"hypertensie","category_label":"Hypertensie","professions":["cardioloog"],"tags":[],"journal":"Journal of the American College of Cardiology","doi":"10.1016/j.jacc.2018.08.2201","source_url":"https://doi.org/10.1016/j.jacc.2018.08.2201","authors":["Konstantinos Dimopoulos","Robin Condliffe","Robert M R Tulloh","Paul Clift","Rafael Alonso-Gonzalez","Radwa Bedair","Natali A Y Chung","Gerry Coghlan","Samantha Fitzsimmons","Alessandra Frigiola","Luke S Howard","Petra Jenkins","Damien Kenny","Wei Li","Simon T MacDonald","Colm McCabe","James J Oliver","Mark S Spence","Gergely V Szantho","Kate von Klemperer","Dirk G Wilson","Stephen J Wort"],"significance":6,"published":"2018-12-04","source_date":"2018-12-04","image":"","kennis":[],"congress":"","summary_en":"This JACC review addressed echocardiographic screening for pulmonary hypertension in patients with congenital heart disease, providing guidance for a population at particularly high risk for developing PH.","created":"2026-07-03T10:27:39Z","updated":"2026-07-03T13:26:52Z","licence":"Citeer vrij, met bronvermelding en een link naar hartvaat.nl (de url van het record). Samenvattingen zijn redactioneel werk van HartVaat; de oorspronkelijke publicaties blijven van hun uitgevers (doi). Geen medisch advies.","body_markdown":"JACC review over echocardiografische screening op pulmonale hypertensie bij patiënten met aangeboren hartafwijkingen.","abstract_original":"Echocardiography is the mainstay in screening for pulmonary hypertension (PH). International guidelines suggest echocardiographic parameters for suspecting PH, but these may not apply to many adults with congenital heart disease (ACHD). PH is relatively common in ACHD patients and can significantly affect their exercise capacity, quality of life, and prognosis. Identification of patients who have developed PH and who may benefit from further investigations (including cardiac catheterization) and treatment is thus extremely important. A systematic review and survey of experts from the United Kingdom and Ireland were performed to assess current knowledge and practice on echocardiographic screening for PH in ACHD. This paper presents the findings of the review and expert statements on the optimal approaches when using echocardiography to assess ACHD patients for PH, with particular focus on major subgroups: patients with right ventricular outflow tract obstruction, patients with systemic right ventricles, patients with unrepaired univentricular circulation, and patients with tetralogy of Fallot with pulmonary atresia."}