{"id":"849833b0aa73","type":"article","url":"https://hartvaat.nl/2026/02/24/aortacoarctatie-met-zeldzame-congenitale-afwijkingen-casuistiek/","title":"Aortacoarctatie met zeldzame congenitale afwijkingen: casuïstiek","title_en":"Rebuttal: aortic coarctation and concomitant anomalies - left circumflex fistula, persistent left SVC and ventricular diverticulum.","category":"hypertensie","category_label":"Hypertensie","professions":["cardioloog"],"tags":["aortacoarctatie","congenitale-hartafwijking"],"journal":"BMJ case reports","doi":"10.1136/bcr-2025-265520","source_url":"https://doi.org/10.1136/bcr-2025-265520","authors":["Abrar Alameri","Ahmed Sherif"],"significance":2,"published":"2026-02-24","source_date":"2026-02-24","image":"","kennis":["https://hartvaat.nl/kennis/nierziekte/nierziekte-en-cardiovasculair-risico/","https://hartvaat.nl/kennis/preventie/preventie-bij-diabetes/"],"congress":"","summary_en":"A case report of an adolescent with aortic coarctation accompanied by rare congenital anomalies including a left circumflex coronary fistula, persistent left superior vena cava, and ventricular diverticulum.","created":"2026-07-03T10:25:09Z","updated":"2026-07-03T13:24:36Z","licence":"Citeer vrij, met bronvermelding en een link naar hartvaat.nl (de url van het record). Samenvattingen zijn redactioneel werk van HartVaat; de oorspronkelijke publicaties blijven van hun uitgevers (doi). Geen medisch advies.","body_markdown":"Coarctatie van de aorta komt voor bij 6 per 1000 levendgeborenen en kan geassocieerd zijn met zeldzame cardiovasculaire anomalieën. Deze casus beschrijft een adolescent met aortacoarctatie, een linkscircumflex-fistel, persisterende linkse vena cava superior en een ventrikeldivertikel.","abstract_original":"Coarctation of the aorta (COA) is a relatively common cardiovascular congenital anomaly. It can be seen in up to 6 per 1000 live births. Rare cardiovascular anomalies have been found to be associated with COA, which may complicate management. We present a case of an adolescent male, incidentally found to be hypertensive. COA was confirmed on imaging, however, with multiple anomalies with an incidence in the general population as common as 0.4 per cent to as rare as 7 cases ever reported in the literature. The association of COA with left circumflex to coronary sinus fistula, ventricular diverticulum and persistent left superior vena cava has never been reported to our knowledge."}